Esferocitosis hereditaria. Carolina Cózar Trastorno hemolítico familiar caracterizado por: anemia ictericia intermitente esplenomegalia. Esferocitosis Hereditaria Anemia Esferocitosis Hereditaria 1) Defecto de la membrana del eritrocito. 2) Retención selectiva por el bazo normal. De esta forma es posible el rastreo de la esferocitosis hereditaria y de la Las manifestaciones clínicas como ictericia, esplenomegalia, anemia, aplasia y y sobrecarga de hierro sugiere daño pancréatico por la acumulación, tal como se.

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Referencias -Mayelin Herrera Garcia.

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HS being a hemolytic defect, frequently increased iron overload was not unexpected. Oxygen affinity and compensated hemolysis in hereditary spherocytosis.

Laparoscopic partial vs total splenectomy in children with hereditary spherocytosis. De esta forma es posible el rastreo de la esferocitosis hereditaria y de la esferocitosis secundaria. This explains the discrepancy between these values. Este hecho explica la discrepancia entre estos valores. Int J Pediatr Hematol Oncol ; 2: Postoperative pulmonary embolism in a young female accompanying with Factor V Leiden mutation and hereditary sypherocytosis.


Clinical symptoms such as jaundice, splenomegaly, anemia, aplasia and biliary calculi prompting a diagnosis of HS are in reality rare.

Journal anema Medical Cases. Servicio de ayuda de la revista. Patient and physician should be informed of the presence of HS to avoid misinterpretation of concurrent pathological symptoms.

Hereditary Spherocytosis in Neonates with Hyperbilirubinemia. Br J Haematol ;93 2: Aires, Argentina; 16 2: Splenectomy for hereditary spherocytosis: Bienvenido a siicsalud Contacto Inquietudes.

Se recomienda el monitoreo de glucemia y ferritina. Long-term evaluation of the beneficial effect of subtotal splenectomy for management of hereditary spherocytosis. The Italian survey on hereditary spherocytosis. Polish Academjy of Sciences? The identity of hyperchromic RBC and spherocytes as well as their normal percentage have been previously established. J Thromb Thrombolysis ;17 3: King on esferocitosus of the General Haematology Task Force of the British Committee for Standards in Haematology Guidelines for the diagnosis and management of hereditary spherocytosis.

Abstract Hematological automates using double beam laser diffraction by artificially spherized red blood cells determine both volume and hemoglobin concentration of a very large number of cells, even indicating percentages of aberrant elements.

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Anemia Esferocitosis Hereditaria by Danna flores cuadros on Prezi

Thus it becomes possible to screen for both hereditary and secondary spherocytosis. Monitoring of blood glucose and ferritin is recommended.

Guidelines for the diagnosis and management of hereditary spherocytosis update. Am J Hematol ;57 1: Clinico-hematological profile of hereditary spherocytosis: Revista Cubana Hematol Inmunol Hemoter ;18 1: The high association of HS with both diabetes and iron overload suggest damage seferocitosis the endocrine pancreas by the latter, as it is also seen in genetic hemochromatosis. Erythroid membrane protein defects in hereditary spherocytosis.

Applying criteria such as permanence of an increased percentage of spherocytes, family history, biochemical symptoms of hemolysis and clinical data, we claim a prevalence of generally asymptomatic hereditary spherocytosis HS of 1: A study of 62 Spanish cases.

J Lab Clin Med. Hereditary spherocytosis, esferoctiosis, and chronic pulmonary emboli: